Published: 2022-11-23

Double chambered right ventricle with ruptured sinus of Valsalva: rare entity

Jaya Lalwani, Lokesh Kumar, Rameshwar ., Jagadeesan M.


Valsalva sinus aneurysm (SVAs) and double-chambered right ventricle (DCRV) is an uncommon congenital heart defect and are usually associated with ventricular septal defect (VSD) in 50% to 60% of patient’s population. The current case report had documented a 59 years old hypertensive asymptomatic male with a known case of SVAs presented to our hospital following device closure for 6 months. On examination, the patient was diagnosed to have DCRV induced by SVAs prior to the closure along with other factors. However, to the best of our knowledge, this is the first case report on DCRV induced by SVAs in synergy with other associated multifactors and without VSD among the Indian population.


Cardiac MRI, DCRV, Incidence, RV, SVAs, VSD

Full Text:



Moustafa S, Mookadam F, Cooper L, Adam G, Zehr K, Stulak J. Sinus of Valsalva aneurysms-47 years of a single center experience and systematic overview of published reports. Am J Cardiol. 2007;99:1159-64.

Cil E, Saraclar M, Özkutlu S. Double-chambered right ventricle: experience with 52 cases. Int J Cardiol. 1995;50:19-29.

Nakashima R, Nitta M, Matsumoto K. Unusual double-chambered right ventricle induced by ruptured sinus of Valsalva aneurysm: A case report. J Cardiol Cases. 2020;22(5):234-7.

Suzuki K, Sezai A, Hinoura R, Unosawa S, Tanaka M. Ruptured Valsalva Sinus Aneurysm with Ventricular Septal Defect and Double-Chambered Right Ventricle without Heart Failure: A Case Report. Heart Surg Forum. 2019;22(6): E429-31.

Hu G, Zhu X, Li G, Jiang F, Li J. A Case Report of Double-Chambered Right Ventricle Associated with Subaterial Ventricular Septal Defect and Rupture of Right Coronary Sinus Aneurysm. Echocardiography. 2015;32(9):1438-40.

Jung SH, Yun TJ, Im YM, Park JJ, Song H, Lee JW et al. Ruptured sinus of Valsalva aneurysm: transaortic repair may cause sinus of Valsalva distortion and aortic regurgitation. J Thorac Cardiovasc Surg. 2008;135:1153-8.

Wang ZJ, Zou CW, Li DC, Li HX, Wang AB, Yuan GD et al. Surgical repair of sinus of Valsalva aneurysm in Asian patients. Ann Thorac Surg. 2007; 84:156-60.

Yan F, Huo Q, Qiao J, Murat V, Ma SF. Surgery for sinus of valsalva aneurysm: 27-year experience with 100 patients. Asian Cardiovasc Thorac Ann. 2008;16(5):361-5.

Reichert CL. Ruptured sinus Valsalva aneurysm, a rare cause of heart failure. Neth Heart J. 2008;16:60-61.

Weijerse A, van der Schoot MJ, Maat LP, Bruning TA, Geleijnse ML, Bogers AJ. Cardiac tamponade due to a ruptured aneurysm of the sinus of valsalva. J Card Surg. 2008; 23:256-8.

Ogata T, Kaneko T, Obayashi T, Sato Y, Murai N, Kaki N, Morishita Y. Ruptured Aneurysm of the Sinus of Valsalva with a Double Chambered Right Ventricle in a Jehovah's Witness Patient. Jap J Cardiovascular Surg.1999;317-9.

Arai N, Matsumoto A, Nishikawa N. Beta-blocker therapy improved symptoms and exercise capacity in a patient with dynamic intra-right ventricle. J Am Soc Echocardiogr. 2001;14:650-53.