Inferior vena caval web causing Budd Chiari syndrome
DOI:
https://doi.org/10.18203/2349-3933.ijam20230372Keywords:
Inferior vena cava, Budd Chiari syndrome, Hepatic venous outflow obstructionAbstract
Budd Chiari syndrome (BCS) is a condition resulting from obstruction of hepatic venous outflow at various levels, regardless of the cause of obstruction. Manifestations can range from asymptomatic state to fulminant hepatic failure or cirrhosis depending on how acutely the obstruction developed. IVC web is an unusual yet potentially treatable cause of BCS. This case report throws light on a rare cause of BCS, which is an IVC web and how endovascular technique helped in patient recovery.
References
Murad S, Plessier A, Guerra M, Fabris F, Eapen CE, Bahr MJ, et al. Etiology, management, and outcome of the Budd-Chiari syndrome. Ann Intern Med. 2009;151(3):167-75.
Okuda K. Membranous obstruction of the inferior vena cava (obliterative hepatocavopathy, Okuda). J Gastroenterol Hepatol. 2001;16(11):1179-83.
Sevenet F, Deramond H, Hadengue A, Casadevall N, Delamarre J, Capron JP. Membranous obstruction of the inferior vena cava associated with a myeloproliferative disorder: a clue to membrane formation? Gastroenterology. 1989;97(4):1019-21.
Yang XL, Cheng TO, Chen CR. Successful treatment by percutaneous balloon angioplasty of Budd-Chiari syndrome caused by membranous obstruction of inferior vena cava: 8-year follow-up study. J Am Coll Cardiol. 1996;28(7):1720-4.
Huang Q, Shen B, Zhang Q, Xu H, Zu M, Gu Y, et al. Comparison of Long-Term Outcomes of Endovascular Management for Membranous and Segmental Inferior Vena Cava Obstruction in Patients With Primary Budd-Chiari Syndrome. Circ Cardiovasc Interv. 2016;9(3):e003104.
Srinivasan P, Rela M, Prachalias A, Muiesan P, Portmann B, Mufti GJ, et al. Liver transplantation for Budd-Chiari syndrome. Transplantation. 2002;73(6):973-7.
Kavanagh PM, Roberts J, Gibney R, Malone D, Hegarty J, McCormick PA. Acute Budd-Chiari syndrome with liver failure: the experience of a policy of initial interventional radiological treatment using transjugular intrahepatic portosystemic shunt. J Gastroenterol Hepatol. 2004;19(10):1135-9.
Mentha G, Giostra E, Majno PE, Bechstein WO, Neuhaus P, O'Grady J, et al. Liver transplantation for Budd-Chiari syndrome: A European study on 248 patients from 51 centres. J Hepatol. 2006;44(3):520-8.