Unilateral pulmonary artery agenesis diagnosed in adulthood: a case report

Veena Charishma R. P.; Sushmita Vinod; Gangadharan Vadivelu; Anbumaran P. Mani

doi:10.18203/2349-3933.ijam20231027

Authors

Veena Charishma R. P. Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India
Sushmita Vinod Saveetha Medical College and Hospital
Gangadharan Vadivelu Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India
Anbumaran P. Mani Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India

DOI:

https://doi.org/10.18203/2349-3933.ijam20231027

Keywords:

Unilateral pulmonary artery agenesis, Tuberculosis, Haemoptysis

Abstract

Isolated pulmonary artery agenesis (UPAA) diagnosed in adulthood is a rare congenital anomaly. It occurs during embryological development where there is a fusion failure between sixth aortic arch and pulmonary truck of affected side. Here we report a case of an adult patient with isolated unilateral right pulmonary artery aplasia.

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