Unilateral pulmonary artery agenesis diagnosed in adulthood: a case report


  • Veena Charishma R. P. Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India
  • Sushmita Vinod Saveetha Medical College and Hospital
  • Gangadharan Vadivelu Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India
  • Anbumaran P. Mani Department of Respiratory Medicine, Saveetha Medical College, Chennai, Tamil Nadu, India




Unilateral pulmonary artery agenesis, Tuberculosis, Haemoptysis


Isolated pulmonary artery agenesis (UPAA) diagnosed in adulthood is a rare congenital anomaly. It occurs during embryological development where there is a fusion failure between sixth aortic arch and pulmonary truck of affected side. Here we report a case of an adult patient with isolated unilateral right pulmonary artery aplasia.



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Case Reports