Eight-and-a-half syndrome in pontine cavernoma: a rare presentation

Authors

  • Shruti M. Nair Department of Ophthalmology, Jawaharlal Institute of Postgraduate education and Medical Research, Pondicherry, India
  • Nirupama Kasturi Department of Ophthalmology, Jawaharlal Institute of Postgraduate education and Medical Research, Pondicherry, India
  • Jayasri P. Department of Ophthalmology, Jawaharlal Institute of Postgraduate education and Medical Research, Pondicherry, India
  • Mary Stephen Department of Ophthalmology, Jawaharlal Institute of Postgraduate education and Medical Research, Pondicherry, India

DOI:

https://doi.org/10.18203/2349-3933.ijam20233573

Keywords:

Horizontal gaze palsy, Internuclear ophthalmoplegia, Facial palsy, Cavernoma, Tarsorrhaphy

Abstract

Cavernous vascular anomalies are varied in form, and cavernomas are very rare lesions commonly found in the supra-tentorial region. Eight-and-a-half syndrome includes horizontal gaze palsy, internuclear ophthalmoplegia, and facial nerve palsy, which is rare in clinical practice. Etiologies are commonly infarct and demyelination. Cavernomas are space-occupying lesions that can lead to life-threatening complications due to haemorrhage, and cavernomas resulting in "eight-and-a-half syndrome" are extremely rare. We report a case of pontine cavernoma presenting as "eight and half syndrome," which worsened systemically, but with timely intervention, the patient recovered completely with good follow-up and an intact permanent tarsorrhaphy.

References

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Published

2023-11-24

Issue

Section

Case Reports