Combined type IV A and type III choledochal cysts associated with autosomal dominant polycystic kidney disease in an adult
Keywords:Choledochal cyst, Biliary tract, Polycystic kidney disease, Cholangitis, Choledochocele
Combination of different types of choledochal cysts are very rare, seldom reported in literature. Their association with polycystic kidney disease has been never reported before. Caroli’s disease is the most commonly associated fibrocystic disease with polycystic kidney disease. Here, we present an a middle aged woman, in whom, evaluation for chronic dyspepsia led to diagnosis of Type IVa and Type III (Choledochocele) associated with polycystic kidney disease, a combination that has never been reported before.
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