Evan’s syndrome a strange cause of hemolysis: a case report
Keywords:
Idiopathic thrombocytopenia purpura, Thrombocytopenia, Autoimmune hemolytic anemiaAbstract
Evan’s Syndrome is an autoimmune disorder characterized by autoimmune hemolytic anemia and Idiopathic Thrombocytopenia Purpura (ITP) or immune neutropenia in absence of any cause. We report this rare autoimmune disorder in a 37 year old female where she had presented with complaints of bleeding per vagina since 7 days with clots, non painful, bilateral joint pain since 2 days, swelling of foot & puffiness of face since 1 day, shortness of breath and pallor. Based on her past history and laboratory investigations confirmed the diagnosis of Evan’ Syndrome. Therapy was initiated with corticosteroids and IV immunoglobulin.
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