Hydroa vacciniforme: a very rare photodermatosis


  • K. S. Dhillon Department of Dermatology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Tarunveer Singh Department of Dermatology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Deepak Sharma Department of Dermatology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • K. R. Varshney Department of Microbiology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Nikha Garg Department of Dermatology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Priyanka Priya Department of Psychiatry, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Uroos Fatima Department of Pathology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India
  • Simmi Chawla Department of Ophthalmology, Era’s Lucknow Medical College, Lucknow, Uttar Pradesh, India


Hydroa vacciniforme, Photodermatosis


Hydroa Vacciniforme (HV) is a rare, acquired and chronic paediatric disorder that is characterized by photosensitivity and recurrent crops of skin lesions on sun-exposed skin, such as the face, ears and hands that heal with vacciniforme scarring. The pathogenesis of HV is unknown. No chromosome abnormality has been identified so far. HV patients have no abnormal laboratory results. The histopathologic features are distinctive and demonstrate intraepidermal multilocular vesicles and cellular necrosis. Most cases remit spontaneously by late adolescence.


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