DOI: http://dx.doi.org/10.18203/2349-3933.ijam20171066

Recurrent self-healing painful ecchymoses and fever: a case of Gardner-diamond syndrome

Sachanidou M. G., Arampatzis G. D., Zioga A., Gaitanis G., Ioannis D. Bassukas

Abstract


Gardner - Diamond syndrome (GDS) is a rare recurrent condition of painful ecchymoses without apparent eliciting factors. We report a 40-year old woman with GDS without psychiatric comorbidity. She presented with, recurrent episodes of spontaneous, self-limiting corps of painful ecchymotic bruising and fever. Her medical history, physical and psychiatric examinations, a focused imaging work up and bone marrow biopsy were unremarkable; the skin biopsy excluded vasculitis. However, the erythrocyte autosensitization test was positive; a finding that together with history and clinico-laboratory results highly suggests GDS.

Keywords


Erythrocyte autosensitization test, Eryptosis, GDS

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References


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